Miller-Dieker syndrome with ring chromosome 17.

نویسندگان

  • N Sharief
  • J Craze
  • D Summers
  • L Butler
  • C B Wood
چکیده

A girl presented at 6 weeks of age with failure to thrive and arching of the back. She had various dysmorphic features, hepatosplenomegaly, and developmental delay. The electroencephalogram and cranial ultrasound were abnormal, and a computed tomogram showed lissencephaly and apparent agenesis of the corpus callosum. Because of frequent aspiration she became oxygen dependent. She later developed intractable convulsions and died at the age of 9 months.

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Clinical commentary with video sequences Ring chromosome 17 epilepsy may resemble that of ring chromosome 20 syndrome

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Human chromosome 17 NotI linking clones and their use in long-range restriction mapping of the Miller-Dieker chromosome region (MDCR) in 17p13.3.

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عنوان ژورنال:
  • Archives of disease in childhood

دوره 66 6  شماره 

صفحات  -

تاریخ انتشار 1991